Hypoplastic Ventricles

Hypoplastic Left Heart Syndrome (HLHS) is a group of congenital malformations characterized by significant underdevelopment of the left side of heart, including: the left ventricle, left atrium, aortic and the mitral valves.

Pulmonary atresia with intact ventricular septum (PA-IVS) encompasses a group of cardiac anomalies that have in common a complete obstruction of the right ventricular outflow tract secondary to an absence of pulmonary valve development, and the presence of a complete interventricular septum.

Double inlet single ventricle is a severe congenital heart disease where a functionally univentricular heart exists.  In this condition the two atria connect totally or predominantly to a single ventricle, the dominant ventricle, which maintains systemic and pulmonary circulation.